Concept information
Preferred term
haemophagocytic lymphohistiocytosis
Definition
- Hemophagocytic lymphohistiocytosis (HLH), also known as haemophagocytic lymphohistiocytosis (British spelling), and hemophagocytic or haemophagocytic syndrome, is an uncommon hematologic disorder seen more often in children than in adults. It is a life-threatening disease of severe hyperinflammation caused by uncontrolled proliferation of activated lymphocytes and macrophages, characterised by proliferation of morphologically benign lymphocytes and macrophages that secrete high amounts of inflammatory cytokines (Wikipedia)
Broader concept
Entry terms
- haemophagocytic syndrome
- macrophage activation syndrome
Creator
- Patricia Fener
In other languages
-
French
-
syndrome d'activation macrophagique
URI
http://data.loterre.fr/ark:/67375/C0X-W2NJR08M-X
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