Concept information
Término preferido
haemophagocytic lymphohistiocytosis
Definición
- Hemophagocytic lymphohistiocytosis (HLH), also known as haemophagocytic lymphohistiocytosis (British spelling), and hemophagocytic or haemophagocytic syndrome, is an uncommon hematologic disorder seen more often in children than in adults. It is a life-threatening disease of severe hyperinflammation caused by uncontrolled proliferation of activated lymphocytes and macrophages, characterised by proliferation of morphologically benign lymphocytes and macrophages that secrete high amounts of inflammatory cytokines (Wikipedia)
Concepto genérico
Etiquetas alternativas
- haemophagocytic syndrome
- macrophage activation syndrome
Creador
- Patricia Fener
En otras lenguas
-
francés
-
syndrome d'activation macrophagique
URI
http://data.loterre.fr/ark:/67375/C0X-W2NJR08M-X
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