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... > Nervous System Diseases > Central Nervous System Diseases > Brain Diseases > Basal Ganglia Diseases > Multiple System Atrophy > Olivopontocerebellar Atrophies
Nervous System Diseases > Central Nervous System Diseases > Movement Disorders > Multiple System Atrophy > Olivopontocerebellar Atrophies
Nervous System Diseases > Autonomic Nervous System Diseases > Primary Dysautonomias > Multiple System Atrophy > Olivopontocerebellar Atrophies
... > Nutritional and Metabolic Diseases > Metabolic Diseases > Proteostasis Deficiencies > Synucleinopathies > Multiple System Atrophy > Olivopontocerebellar Atrophies
Nervous System Diseases > Neurodegenerative Diseases > Synucleinopathies > Multiple System Atrophy > Olivopontocerebellar Atrophies
... > Nervous System Diseases > Central Nervous System Diseases > Brain Diseases > Cerebellar Diseases > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Nervous System Diseases > Central Nervous System Diseases > Spinal Cord Diseases > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Genetic Diseases, Inborn > Heredodegenerative Disorders, Nervous System > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies
Nervous System Diseases > Neurodegenerative Diseases > Heredodegenerative Disorders, Nervous System > Spinocerebellar Degenerations > Olivopontocerebellar Atrophies

Preferred term

Olivopontocerebellar Atrophies  

Type

  • mesh:Descriptor

Definition

  • A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)

Broader concept

Entry terms

  • Dejerine-Thomas Syndrome
  • Olivo-Ponto-Cerebellar Atrophy
  • Olivopontocerebellar Atrophy
  • Olivo-Ponto-Cerebellar Degeneration
  • Olivopontocerebellar Degeneration
  • Pontoolivocerebellar Atrophy
  • Presenile Ataxia

Allowable Qualifier(s)

In other languages

  • Atrophies olivo-ponto-cérébelleuses

    French

  • AOPC
  • Atrophie olivo-ponto-cérébelleuse
  • Atrophie olivopontocérébelleuse
  • Atrophies olivopontocérébelleuses
  • Syndrome de Déjerine-Thomas

URI

http://data.loterre.fr/ark:/67375/JVR-JSVXFCPH-Q

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