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Concept information

Preferred term

Leber Congenital Amaurosis  

Type

  • mesh:Descriptor

Definition

  • A rare degenerative inherited eye disease that appears at birth or in the first few months of life that results in a loss of vision. Not to be confused with LEBER HEREDITARY OPTIC NEUROPATHY, the disease is thought to be caused by abnormal development of PHOTORECEPTOR CELLS in the RETINA, or by the extremely premature degeneration of retinal cells.

Entry terms

  • Amaurosis, Leber Congenital
  • Congenital Retinal Blindness
  • Leber Abiotrophy
  • Leber Congenital Tapetoretinal Degeneration
  • Leber's Amaurosis

In other languages

URI

http://data.loterre.fr/ark:/67375/JVR-QCC3H5R1-3

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RDF/XML TURTLE JSON-LD Created 7/6/09, last modified 7/8/13