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... > Enzymes and Coenzymes > Enzymes > Lyases > Carbon-Oxygen Lyases > Polysaccharide-Lyases > Chondroitinases and Chondroitin Lyases > Chondroitinsulfatases > N-Acetylgalactosamine-4-Sulfatase
... > Enzymes and Coenzymes > Enzymes > Hydrolases > Esterases > Sulfatases > Chondroitinases and Chondroitin Lyases > Chondroitinsulfatases > N-Acetylgalactosamine-4-Sulfatase
... > Enzymes and Coenzymes > Enzymes > Hydrolases > Esterases > Sulfatases > Arylsulfatases > N-Acetylgalactosamine-4-Sulfatase

Preferred term

N-Acetylgalactosamine-4-Sulfatase  

Type

  • mesh:Descriptor

Definition

  • An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.

Broader concept

Entry terms

  • Arylsulfatase B
  • N-Acetyl-D-Galactosamine-4-sulfate 4-sulfohydrolase
  • N-Acetylgalactosamine 4-Sulfatase
  • N-Acetylgalactosamine-4-sulfate Sulfatase
  • N-Acetylgalactosamine-4-sulphate Sulphatase

Allowable Qualifier(s)

In other languages

URI

http://data.loterre.fr/ark:/67375/JVR-RLM770GM-9

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RDF/XML TURTLE JSON-LD Created 6/10/98, last modified 6/28/16