Concept information
Nervous System Diseases
Autonomic Nervous System Diseases
Primary Dysautonomias
Multiple System Atrophy
...
Central Nervous System Diseases
Brain Diseases
Cerebellar Diseases
Spinocerebellar Degenerations
Nervous System Diseases
Central Nervous System Diseases
Spinal Cord Diseases
Spinocerebellar Degenerations
Término preferido
Olivopontocerebellar Atrophies
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Tipo
-
mesh:Descriptor
Definición
- A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)
Concepto genérico
Etiquetas alternativas
- Dejerine-Thomas Syndrome
- Olivo-Ponto-Cerebellar Atrophy
- Olivopontocerebellar Atrophy
- Olivo-Ponto-Cerebellar Degeneration
- Olivopontocerebellar Degeneration
- Pontoolivocerebellar Atrophy
- Presenile Ataxia
En otras lenguas
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francés
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AOPC
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Atrophie olivo-ponto-cérébelleuse
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Atrophie olivopontocérébelleuse
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Atrophies olivopontocérébelleuses
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Syndrome de Déjerine-Thomas
URI
http://data.loterre.fr/ark:/67375/JVR-JSVXFCPH-Q
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