Concept information
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Central Nervous System Diseases
Central Nervous System Infections
Central Nervous System Viral Diseases
Encephalitis, Viral
Infections
Central Nervous System Infections
Central Nervous System Viral Diseases
Encephalitis, Viral
Término preferido
Subacute Sclerosing Panencephalitis
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Tipo
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mesh:Descriptor
Definición
- A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
Concepto genérico
Etiquetas alternativas
- Encephalitis, Inclusion Body, Measles
- Inclusion Body Encephalitis, Measles
- Leukoencephalitis, Subacute Sclerosing
- Leukoencephalitis, Van Bogaert's
- Measles Inclusion Body Encephalitis
- Panencephalitis, Subacute Sclerosing
- Sclerosing Leukoencephalitis, Subacute
- Sclerosing Panencephalitis, Subacute
- SSPE
- Van Bogaert's Leukoencephalitis
En otras lenguas
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francés
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Encéphalite à inclusions
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Encéphalite morbilleuse à inclusions
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LESS
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Leuco-encéphalite sclérosante subaiguë
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Leuco-encéphalite sclérosante subaigüe
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Leucoencéphalite sclérosante subaiguë
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Maladie de Van Bogaert
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Panencéphalite sclérosante subaiguë
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Panencéphalite sclérosante subaigüe
URI
http://data.loterre.fr/ark:/67375/JVR-L9D5LCCL-M
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