Concept information
Digestive System Diseases
Digestive System Neoplasms
Gastrointestinal Neoplasms
Intestinal Neoplasms
Término preferido
Immunoproliferative Small Intestinal Disease
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Tipo
-
mesh:Descriptor
Definición
- A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.
Concepto genérico
Etiquetas alternativas
- alpha-Chain Disease
- Heavy Chain Disease, IgA Type
- IPSID
- Lymphoma, Mediterranean
En otras lenguas
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francés
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IPSID
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Lymphome méditerranéen
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Maladie des chaines alpha
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Maladie des chaînes alpha
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Maladie des chaines lourdes a
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Maladie des chaines lourdes alpha
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Maladie des chaines lourdes d'IgA
URI
http://data.loterre.fr/ark:/67375/JVR-PJR2H5WT-S
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