Concept information
Término preferido
Neoplastic Syndromes, Hereditary
Notice: Undefined index: in /var/www/html/model/Concept.php on line 545
Tipo
-
mesh:Descriptor
Definición
- The condition of a pattern of malignancies within a family, but not every individual's necessarily having the same neoplasm. Characteristically the tumor tends to occur at an earlier than average age, individuals may have more than one primary tumor, the tumors may be multicentric, usually more than 25 percent of the individuals in direct lineal descent from the proband are affected, and the cancer predisposition in these families behaves as an autosomal dominant trait with about 60 percent penetrance.
Concepto genérico
Conceptos específicos
- Adenomatous Polyposis Coli
- Basal Cell Nevus Syndrome
- Birt-Hogg-Dube Syndrome
- Colorectal Neoplasms, Hereditary Nonpolyposis
- Dysplastic Nevus Syndrome
- Exostoses, Multiple Hereditary
- Hamartoma Syndrome, Multiple
- Hereditary Breast and Ovarian Cancer Syndrome
- Li-Fraumeni Syndrome
- Multiple Endocrine Neoplasia
- Neurofibromatoses
- Peutz-Jeghers Syndrome
- Tuberous Sclerosis
- Wilms Tumor
Etiquetas alternativas
- Cancer Syndromes, Hereditary
- Hereditary Cancer Syndromes
- Hereditary Neoplastic Syndromes
En otras lenguas
-
francés
-
Syndromes cancéreux héréditaires
-
Syndromes tumoraux héréditaires
URI
http://data.loterre.fr/ark:/67375/JVR-V2Z38MHB-L
{{label}}
{{#each values }} {{! loop through ConceptPropertyValue objects }}
{{#if prefLabel }}
{{/if}}
{{/each}}
{{#if notation }}{{ notation }} {{/if}}{{ prefLabel }}
{{#ifDifferentLabelLang lang }} ({{ lang }}){{/ifDifferentLabelLang}}
{{#if vocabName }}
{{ vocabName }}
{{/if}}