Passer au contenu principal

Medical Subject Headings (thesaurus)

Choisissez le vocabulaire dans lequel chercher

Concept information

Terme préférentiel

Darier Disease  

Type

  • mesh:Descriptor

Définition

  • An autosomal dominantly inherited skin disorder characterized by warty malodorous papules that coalesce into plaques. It is caused by mutations in the ATP2A2 gene encoding SERCA2 protein, one of the SARCOPLASMIC RETICULUM CALCIUM-TRANSPORTING ATPASES. The condition is similar, clinically and histologically, to BENIGN FAMILIAL PEMPHIGUS, another autosomal dominant skin disorder. Both diseases have defective calcium pumps (CALCIUM-TRANSPORTING ATPASES) and unstable desmosomal adhesion junctions (DESMOSOMES) between KERATINOCYTES. An alleleic variant of Darier's disease.

Synonyme(s)

  • Darier's Disease
  • Darier-White Disease
  • Keratosis Follicularis

Traductions

  • français

  • Dyskératose de Darier
  • Dyskératose folliculaire de Darier
  • Kératose folliculaire
  • Maladie de Darier-White

URI

http://data.loterre.fr/ark:/67375/JVR-H5Z7J9GX-V

Télécharger ce concept :

RDF/XML TURTLE JSON-LD Date de création 01/01/1999, dernière modification le 18/06/2015