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Concept information

Nervous System Diseases > Nervous System Malformations > Hydranencephaly
Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Congenital Abnormalities > Nervous System Malformations > Hydranencephaly

Terme préférentiel

Hydranencephaly  

Type

  • mesh:Descriptor

Définition

  • A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)

Concept générique

Synonyme(s)

  • Absence of Cerebral Hemispheres, Congenital
  • Cerebral Hemispheres, Absence, Congenital
  • Congenital Absence of Cerebral Hemispheres

Qualificatif(s) autorisé(s)

Traductions

URI

http://data.loterre.fr/ark:/67375/JVR-L2WQG382-P

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RDF/XML TURTLE JSON-LD Date de création 01/01/1999, dernière modification le 30/07/2005