Concept information
Término preferido
Klippel-Trenaunay angiodysplasia
Definición
- Klippel–Trénaunay syndrome formerly Klippel–Trénaunay–Weber syndrome and sometimes angioosteohypertrophy syndrome and hemangiectatic hypertrophy, is a rare congenital medical condition in which blood vessels and/or lymph vessels fail to form properly. The three main features are nevus flammeus (port-wine stain), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. It is similar to, though distinctly separate from, the less common Parkes-Weber syndrome. The classical triad of Klippel-Trenaunay syndrome consists of: vascular malformations of the capillary, venous and lymphatic vessels; varicosities of unusual distribution, particularly the lateral venous anomaly; and unilateral soft and skeletal tissue hypertrophy, usually the lower extremity. (Wikipedia)
Concepto genérico
Etiquetas alternativas
- Klippel-Trenaunay syndrome
En otras lenguas
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francés
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maladie de Klippel-Trenaunay
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syndrome de Klippel-Trenaunay
URI
http://data.loterre.fr/ark:/67375/VH8-LMXZDPVZ-J
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